N-Isovalerylglycine is a useful diagnostic tool in the diagnosis of many organic acidemias and mitochondrial fatty acid β-oxidation defects. N-Isovalerylglycine is found in the urine of patients with isovaleric acidemia, an inborn error of leucine metabolism.
SKU | RCLST006719 |
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CAS number | 16284-60-9 |
Molecular Formula | C7H13NO3 |
Catalog Number | RCLST006719 |
Chemical Name | N-Iso Valerylglycine |
Synonyms | N-(3-Methyl-1-oxobutyl)glycine; N-Isovalerylglycine; Isovalerylglycine; N-Isovaleroylglycine; |
Molecular Weight | 159.18 |
Solubility | DMSO (Slightly), Methanol (Slightly) |
Stability | No Data Available |
Appearance | White to Off-White Solid |
Storage Condition | Refrigerator |